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Question: 20120070
Status
Final

References
Source 1:   2012 Heme & Lymph Manual & DB
pgs:  
Notes:  
Source 2:  
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Notes:  


Question
Multiple primaries--Heme & Lymphoid Neoplasms: Should myelofibrosis be coded as a second primary, or is it a descriptor of the MDS/RAEB-2?

See discussion.

Discussion
This is a bone marrow diagnosis: High-grade myelodysplastic syndrome - refractory anemia with excess blasts type 2 (RAEB-2) and myelofibrosis

The multiple primaries calculator shows for 9983/3 and 9961/3 this is a new primary, but I'm not sure if I'm interpreting this correctly.

Answer
Code a single primary, RAEB 9983/3.

Code 9961/3 is for PRIMARY myelofibrosis. Myelofibrosis, NOS (not specified as primary myelofibrosis) is not reportable. Myelofibrosis means a proliferation of fibroblastic cells in bone marrow, causing anemia and sometimes enlargement of the spleen and liver. Myelofibrosis may be associated with both benign and malignant disease processes.

History


Last Updated
08/29/2012

Date Finalized
08/29/2012