SEER Inquiry System - View
Source 1: 2012 Heme & Lymph Manual & DB
Reportability-Heme & Lymphoid Neoplasms: Is Mast Cell Activation Syndrome(MCAS)reportable? Our coders are giving it an ICD-9 code of 202.60, but the doctors say in the progress note that it is not the same as systemic mastocytosis. I can't find a listing for MCAS in the Hematopoietic and Lymphoid Database.
MACS is not reportable as a neoplam unless it is specifically stated to be a result of a mast cell proliferative disorder which we do report.
We consulted with our expert pathologist on this issue. MACS is a relatively new term used for conditions in which patients experience the symptoms of mast cell mediators in the absence of an increase/proliferation of mast cells. The diagnosis of this group of disorders is based in part on a complex of symptoms and on the demonstration of no increase in mast cells.
Some of these diseases are difficult to separate from mastocytosis (which is reportable), but for the time being, this group of disorders is not considered part of the systemic mastocytosis/mast cell leukemia/mast cell sarcoma spectrum.