SEER Inquiry System - View

Question: 20130073 Status
Final

References
Source 1:   ICD-O-3
pgs:  
Notes:  
Source 2:  
pgs:  
Notes:  


Question
Reportability--Brain and CNS: Is Rosai-Dorfman disease considered a neoplastic reportable disease process if it occurs in the brain? See Discussion.

Discussion
The pathology report diagnosis is: Cranium, right temporal area, resection of intradural, extra-axial mass: Severe acute and chronic inflammation, histiocytic reaction, and proliferative fibrosis. See comment.

Comment: Among potential alternative considerations are an infectious process, or non-infectious inflammatory CNS lesions such as inflammatory pseudotumor, Rosai-Dorfman disease, plasma cell granuloma, idiopathic hypertrophic pachymeningitis, and inflammatory myofibroblastic tumor.

The clinicians discuss this and review other chart information and conclude the patient has a clinical diagnosis of Rosai-Dorfman disease.

This is a rare disorder characterized by proliferation of histiocytes.

Answer
This case is not reportable. Rosai-Dorfman disease is not listed in the ICD-O-3. To be reportable, a neoplasm must be listed in the ICD-O-3 and originate in a reportable brain/CNS site.

History


Last Updated
06/24/2014

Date Finalized
07/31/2013