Lymphocyte-rich classical Hodgkin lymphoma

Name
Lymphocyte-rich classical Hodgkin lymphoma
ICD-O-3 Morphology
9651/3
Effective 2001 and later
Reportable
for cases diagnosed 2001 and later
Primary Site(s)
C770-C779

Help me code for dx year :

Grade
Code grade specified by pathologist. If no grade specified, code 9
Module Rule
None
Alternate Names
Hodgkin disease, lymphocyte predominance, NOS [OBS]
Hodgkin disease, lymphocytic-histiocytic predominance [OBS]
Hodgkin disease, lymphocytic-predominance, diffuse [OBS]
Hodgkin lymphoma, lymphocyte-rich
LR-cHL
LRCHL
Definition
Subtype of classical hodgkin lymphoma characterized by background of abundant small lymphocytes. Reed-Sternberg cells have classic morphology and immunophenotype. Most common growth pattern nodular, diffuse pattern rarely seen. 40% associated with EBV.

Lymphocyte-rich classical Hodgkin lymphoma is a subtype of classical Hodgkin lymphoma with scattered Hodgkin and Reed-Sternberg cells with a nodular or less often diffuse cellular background consisting of small lymphocytes and an absence of neutrophils and eosinophils.
Abstractor Notes
Lymphocyte-rich classical Hodgkin lymphoma (LRCHL) typically involves peripheral lymph nodes. Mediastinal involvement and bulky disease are uncommon. Most patients present with stage I or II disease. B symptoms are rare. The clinical features are similar to those of NLPHL with the exception that multiple relapses seem to occur less frequently. With modern risk-adjusted treatment, survival and progression free survival are slightly better than the other subtypes of CHL.

Preferred primary sites are listed for this disease in the primary site field; however, involvement in other sites is possible, but rare. If you have confirmation that the only involved site is something other than the preferred primary listed, then code to that primary site.
Definitive Diagnostic Methods
Histologic confirmation
Immunophenotype
Genetics Data
None
Immunophenotyping
CD15+/-
CD20+/-
CD30+
CD45-
CD75-
J chain-
Treatments
Chemotherapy
Hormone
Radiation
Corresponding ICD-9 Codes
201.4 Lymphocytic-histiocytic predominance
Corresponding ICD-10 Codes
C81.7 Other Hodgkin's disease
Corresponding ICD-10-CM Codes (effective October 1, 2015 U.S. only)
C81.4 Lymphocyte-rich classical Hodgkin lymphoma
Signs and Symptoms
None
Diagnostic Exams
None
Recurrence and Metastases
None
Epidemiology and Mortality
None