Question: 20170073

Status


Final

Category


#1:   Histology
#2:   Behavior
#3:   Brain and CNS


References


Source 1:   WHO Class CNS Tumors
pgs:   177
Notes:   4th edition
Source 2:   ICD-O-3
pgs:  
Notes:  


Question


Histology/Behavior--Brain and CNS: How are histology and behavior coded for a diagnosis of pineal anlage tumor in an infant? See Discussion.


 



Discussion


Patient is an 11 month old with brain biopsy showing final diagnosis of pineal anlage tumor. How are behavior and histology coded for this rare tumor?



Answer


Assign 9362/3 for pineal anlage tumors.  According to the WHO Classification of Tumors of the Central Nervous System, 4th edition, pineal anlage tumors, while extremely rare, share features with pineoblastoma. Although they have a distinct morphology, there is no other ICD-O-3 code for pineal anlage tumors.



History




Last Updated


10/26/2017

Date Finalized


01/10/2018