Question: 20190002

Status


Final

Category


#1:   Histology
#2:   Behavior
#3:   Brain and CNS


References


Source 1:   Subject matter expert
pgs:  
Notes:  
Source 2:  
pgs:  
Notes:  


Question


Histology/Behavior--Brain and CNS: How should Histology and Behavior be coded for a polymorphous low-grade neuroepithelial tumor of the young (PLNTY) arising in the brain?



Discussion




Answer


Assign code 9505/1 for ganglioglioma.  Per our expert neuropathologist, according to the paper that has done the most work on PLNTY cases, it appears most closely related to the ganglioglioma. It is surely a neoplasm as it has recurrent mutations and fusions seen in other tumors, again, most like gangliogliomas.



History




Last Updated


01/02/2019

Date Finalized


02/14/2019