Source 1: 2012 Heme & Lymph Manual & DB
Reportability--Hem & Lymphoid Neoplasms: This pt was diagnosed with “Hemophagocytic lymphohistiocytosis” on blood & bone marrow biopsy. Other doctors also called this “Hemophagocytosis” or “hemophagocytic syndrome”. This appears in database as 9724.3. This pt had several rounds of fairly aggressive chemo. Is this still not reportable? If it is, what site do I code?
I had trouble collaborative staging this site & got several conflicting edit errors. I originally had site as C421 (BM BX). Histology is not included in Heme schema. Tried to use other ill-defined schema; got error. Ended up changing site to C779 LN, NOS to use Hodgkins schema to clear edits. Is it correct to code 9724.3 to C779 instead of C421?
See SINQ # 20100113.
Hemophagocytic sydrome is not reportable. This disease is also known as hemophagocytic lymphohistiocytosis (HLH). HLH is caused by an over-stimulated immune system (infection, etc.) It is a clinical syndrome that is associated with a variety of underlying conditions.
Systemic EBV-positive T-cell lymphoproliferative disease of childhood 9724/3 is not applicable. To use 9724, the patient must be a child, and there must be documentation of FULIMINANT hemophagocytic syndrome in the patient.