Fibroblastic reticular cell tumor

Name
Fibroblastic reticular cell tumor
ICD-O-3 Morphology
9759/3
Effective 2010 and later
Reportable
for cases diagnosed 2010 and later
Primary Site(s)
See Abstractor Notes

Help me code for dx year :

Grade
9 - Grade/differentiation unknown, not stated, or not applicable
Module Rule
None
Alternate Names
Cytokeratin-positive interstitial reticulum cell tumor
Definition
This tumor is very rare and may also be is reported as "cytokeratin-positive interstitial reticulum cell tumor". The tumor is histologically similar to follicular dendritic cell sarcoma or Interdigitating dendritic cell sarcoma (9757/3), but lacks the immunophenotypic profile of these tumor types. It derives from stroma-derived dendritic cells.
Abstractor Notes
(This code is effective for cases diagnosed 2010 and later.) Fibroblastic reticular cell tumor is extremely rare. This neoplasm can manifest in lymph nodes, spleen, or soft tissue. The clinical outcome is variable with some patients dying of the disease. The tumor is similar to follicular dendritic cell sarcoma (9758/3) and Interdigitating dendritic cell sarcoma (9757/3) but lacks the immunophenotypic profile of these tumor types.
Definitive Diagnostic Methods
Histology
Genetics Data
None
Immunophenotyping
Variable reactivity for smooth muscle actin, desmin, cytokeratin (dendritic pattern) and CD68
Treatments
Chemotherapy
Radiation
Surgery
Transformations to
None
Transformations from
None
Same Primaries
None
Corresponding ICD-9 Codes
202.9 Other and unspecified malignant neoplasms
Corresponding ICD-10 Codes
C96.7 Other specified malignant neoplasms of lymphoid, hematopoietic
Corresponding ICD-10-CM Codes (effective October 1, 2015 U.S. only)
C96.4 Sarcoma of dendritic cells (accessory cells)
Signs and Symptoms
None
Diagnostic Exams
None
Recurrence and Metastases
None
Epidemiology and Mortality
None