SEER is an authoritative source of information on cancer incidence and survival in the United States. SEER currently collects and publishes cancer incidence and survival data from population-based cancer registries covering approximately 28 percent of the U.S. population.
(This code is effective for cases diagnosed 2010 and later. For cases diagnosed prior to 2010 see code 9702/3).
Hydroa vacciniforme-like lymphoma is one of two major types of Epstein-Barr (EBV) associated T-celllymphoproliferative disorders that have been reported in the pediatric age group. (See also 9724/3: Systemic EBV-positive T-celllymphoproliferative disease of childhood)
The neoplastic cells are generally small to medium in size without significant atypia. The infiltrates show extension from the epidermis to the subcutis, showing necrosis, angiocentricity and angioinvasion. The overlying epidermis is frequently ulcerated.
Systemic spread and mosquito bite allergy/hypersensitivity result in a much more aggressive clinical course.
This disease is treated with UV (ultra-violet light) or PUVA (psoralen plus ultraviolet light). UV and PUVA are both coded as "Other Treatment."