Lymphomatoid papulosis

This disease is not reportable.
Name
Lymphomatoid papulosis
ICD-O-3 Morphology
9718/1
Effective 2010 and later
Reportable
This disease is not reportable
Primary Site(s)
See Abstractor Notes
Alternate Names
LyP
Definition
Lymphomatoid papulosis (LyP) is a chronic, recurrent, self-healing skin disease composed of large atypical anaplastic, immunoblastic or Hodgkin-like cells in a marked inflammatory background. In some cases the pattern of cutaneous involvement may resemble MF (type B). This neoplasm is a /3 in ICD-O-3 but was changed to a /1 in the 2001 and 2009 WHO classification. The pending ICD-O-3 errata has also changed the behavior code to a /1. This is part of the primary cutaneous CD30 positive T-cell lymphoproliferative disorders WHO group, which also includes Primary cutaneous anaplastic large cell lymphoma (see 9718/3).
Immunophenotyping
CD 8 neg
CD3+
CD4+
Corresponding ICD-9 Codes
709.8 Other specified disorders of skin
Corresponding ICD-10 Codes
L41.2 Lymphomatoid papulosis
Corresponding ICD-10-CM Codes (effective October 1, 2015 U.S. only)
C86.6 Primary cutaneous CD30-positive T-cell proliferations