An official website of the United States government
Home
SEER Inquiry System - Report
Produced: 10/14/2025 5:31 AM
Question 20200085
Inquiry Details
References:
#1: Solid Tumor Rules. Head and Neck; December 2020 Update
#2: ICD-O-3.2 Update for 2021. NAACCR Implementation Guidelines
Question:
Solid Tumor Rules (2018)/Histology--Head and Neck: What is the histology of paraganglioma, NOS arising outside of the adrenal gland (for example, in the bladder) for cases diagnosed 1/1/2021 and later? See Discussion.
Discussion:
Should histology be coded as paraganglioma, NOS (8680/3) or as extra-adrenal paraganglioma, NOS (8693/3) for a diagnosis of paraganglioma in the bladder? Does the pathologist have to specifically diagnose the tumor as extra-adrenal paraganglioma, NOS to use histology code 8693/3? Or, does any diagnosis of paraganglioma (NOS) arising outside of the adrenal gland, carotid body, middle ear, or aortic body (the specified sites for other types of paragangliomas) qualify as an extra-adrenal paraganglioma, NOS?
The ICD-O-3.2 Implementation Guidelines (Tables 6 and 7) provide an associated site of C755 for histology 8680/3 (paraganglioma, NOS), but no associated site code is provided for histology 8693/3 (extra-adrenal paraganglioma, NOS). If the preferred site for paraganglioma, NOS is the paraganglia, would a paraganglioma in the bladder be an extra-adrenal paraganglioma?
This question was prompted from preparing SEER*Educate coding exercises. We will use the answer as a reference in the rationales.
Answer:
Code the histology stated by the pathologist: paraganglioma, NOS 8680/3.
