Name

Extramammary Paget disease

This definition applies to

All SEER websites where this term appears

Definition

Extramammary Paget disease (EMPD) is characterized by a chronic eczema-like rash of the skin around the genital regions of males and females. Under the microscope, this condition looks very similar to a condition that occurs on the breast called mammary Paget disease. The primary difference between the two is the location of the rash. While the location of the rash for individuals with mammary Paget disease is around the nipple and areolar skin, EMPD may occur in the vulva, perianal region, scrotum, penis, and axilla. About 25 percent of Extramammary Paget disease is associated with an underlying cancer.

Resource

Title: National Institutes of Health
Genetic and Rare Diseases Information Center

Alternate Names

None

Abstractor Notes

None

Histology

8542/3: Extramammary Paget disease (except Paget disease of bone)

Primary Sites

None
Glossary