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This neoplasm is not reportable.
Name
Rosai-Dorfman disease
Reportability
This neoplasm is not reportable
Abstractor Notes
This disease became reportable 1/1/2021 as an alternate name for Erdheim Chester disease (9749/3).
Alternate Names
Sinus histiocytosis with massive lymphadenopathy
Definition
This is a reactive condition of unknown etiology with increased histiocytes. The disease can mimic lymphoma. Extranodal involvement is frequent.
The majority of lesions are self-limited and benign. Rare fatalities have been associated with immunologic disorders, lymphomas of Hodgkin and non-Hodgkin type, leukemias and exceptional cases with solid tumors
The majority of lesions are self-limited and benign. Rare fatalities have been associated with immunologic disorders, lymphomas of Hodgkin and non-Hodgkin type, leukemias and exceptional cases with solid tumors
