This neoplasm is not reportable.

Name

Rosai-Dorfman disease

Not Reportable

This neoplasm is not reportable

Alternate Names

Sinus histiocytosis with massive lymphadenopathy

Definition

This is a reactive condition of unknown etiology with increased histiocytes. The disease can mimic lymphoma. Extranodal involvement is frequent.

The majority of lesions are self-limited and benign. Rare fatalities have been associated with immunologic disorders, lymphomas of Hodgkin and non-Hodgkin type, leukemias and exceptional cases with solid tumors

Abstractor Notes

For more information, see the Histiocytosis Association website (http://www.histio.org/page.aspx?pid=399#.V1cZIUYw0eU)
Glossary