Rosai-Dorfman disease

This neoplasm is not reportable.
Rosai-Dorfman disease
Not Reportable
This neoplasm is not reportable
Alternate Names
Sinus histiocytosis with massive lymphadenopathy
Abstractor Notes
This is a reactive condition of unknown etiology with increased histiocytes. The disease can mimic lymphoma. Extranodal involvement is frequent.

The majority of lesions are self-limited and benign. Rare fatalities have been associated with immunologic disorders, lymphomas of Hodgkin and non-Hodgkin type, leukemias and exceptional cases with solid tumors