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This neoplasm is not reportable.

Name

Mast Cell Activation Syndrome

Reportability

This neoplasm is not reportable

Alternate Names

MCAS

Definition

Group of disorders based on complex of symptoms with no increase in mast cells.

Not part of the systemic mastocytosis/mast cell leukemia/mast cell sarcoma spectrum.

Corresponding ICD-10-CM Codes (U.S. only)

D89.40 Mast cell activation, unspecified (effective October 01, 2015)
D89.41 Monoclonal mast cell activation syndrome (effective October 01, 2015)
D89.42 Idiopathic mast cell activation syndrome (effective October 01, 2015)
D89.43 Secondary mast cell activation (effective October 01, 2015)
D89.49 Other mast cell activation disorder (effective October 01, 2015)

Sources

Swerdlow SH, Campo E, Harris NL, Jaffe ES, Pileri SA, Stein H, Thiele J (Eds):
WHO Classification of Tumours of Haematopoietic and Lymphoid Tissues (Revised 4th edition)
IARC: Lyon 2017
Section: Mastocytosis
Pages: 63
Glossary