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This neoplasm is not reportable.
Abstractor Notes
This is not reportable, not part of the systemic mastocytosis/mast cell leukemia/mast cell sarcoma spectrum.
Alternate Names
MCAS
Definition
"Mast cell activation syndrome (MCAS) is a condition that causes intense episodes of swelling, shortness of breath, hives, diarrhea, vomiting and other symptoms. In severe cases, it may lead to life-threatening anaphylaxis. It’s caused by mast cells (mistakenly) alerting your immune system that there’s something harmful in your body."
Corresponding ICD-10-CM Codes (U.S. only)
D89.40 Mast cell activation, unspecified (effective October 01, 2015)
D89.41 Monoclonal mast cell activation syndrome (effective October 01, 2015)
D89.42 Idiopathic mast cell activation syndrome (effective October 01, 2015)
D89.43 Secondary mast cell activation (effective October 01, 2015)
D89.49 Other mast cell activation disorder (effective October 01, 2015)
Sources
Cleveland Clinic: Health Library. Diseases and Conditions
https://my.clevelandclinic.org/health/diseases/mast-cell-activation-syndrome
https://my.clevelandclinic.org/health/diseases/mast-cell-activation-syndrome
