SEER Hematopoietic and Lymphoid Neoplasm Database

This neoplasm is not reportable.

Name

Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder

ICD-O-3 Morphology

9709/1: Primary cutaneous CD4-positive small/medium T-cell lymphoproliferative disorder

Effective 2021 and later

Reportability

This neoplasm is not reportable

Primary Site(s)

No primary site specified

This neoplasm is reportable for primary sites C700-C729, C751-C753 only.

Abstractor Notes

These lesions usually present as a solitary plaque or nodule, most commonly on the face, neck, or upper trunk. Patients are asymptomatic, a single slow growing skin lesion is the sole manifestation of this disease.

Alternate Names

Primary cutaneous CD4+ small/medium T-cell lymphoma [OBS]

Definition

Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder is characterized by a predominance of small to medium-sized CD4+ pleomorphic T cells and by presentation with a solitary skin lesion in almost all cases, without evidence of the patches and plaques typical of mycosis fungoides.

Because these cases have the same clinicopathological features and benign clinical course as cutaneous pseudo-T-cell lymphomas with a nodular growth pattern, the term primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder is preferred.

Genetics Data

This data item does not apply

Immunophenotyping

This data item does not apply

Corresponding ICD-9 Codes

238.79 Other lymphatic and hematopoietic tissues

Corresponding ICD-10 Codes

D47.7 Other specified neoplasms of uncertain or unknown behavior of lymphoid, hematopoietic, and related tissue

Corresponding ICD-10-CM Codes (U.S. only)

D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue (effective October 01, 2015)

Sources

Swerdlow SH, Campo E, Harris NL, Jaffe ES, Pileri SA, Stein H, Thiele J (Eds):
WHO Classification of Tumours of Haematopoietic and Lymphoid Tissues (Revised 4th edition)
IARC: Lyon 2017
Section: Mature T- and NK-cell neoplasms
Pages: 401-402

International Classification of Diseases for Oncology, Third Edition, Second Revision. Geneva: World Health Organization, 2020
Section: ICD-O-3.2 (2020) Morphological Codes
Pages: http://www.iacr.com.fr/index.php?option=com_content&view=category&layout=blog&id=100&Itemid=577

Glossary