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This neoplasm is not reportable.
Name
ICD-O-3 Morphology
9727/1
Effective
2026 and later
Reportability
This neoplasm is not reportable
Primary Site(s)
No primary site specified
This hematopoietic disease is not reportable for the U.S. except for primary sites C700-C729, C751-C753.
Canada, refer to your specific province for reportability requirements.
Canada, refer to your specific province for reportability requirements.
Abstractor Notes
Mature plasmacytoid dendritic cell proliferation associated with myeloid neoplasm is part of the Plasmacytoid dendritic cell neoplasms lineage table in the WHO 5th edition of Hematolymphoid Tumors. (See Appendix B in the Hematopoietic Manual, Table B10)
Most cases have been described in the skin and bone marrow. Very rarely involves the lymph nodes.
The neoplasm occurs within the context of a myeloid neoplasm, most notably Acute Myeloid Leukemia (AML) or Chronic Myelomonocytic Leukemia (CMML).
Most cases have been described in the skin and bone marrow. Very rarely involves the lymph nodes.
The neoplasm occurs within the context of a myeloid neoplasm, most notably Acute Myeloid Leukemia (AML) or Chronic Myelomonocytic Leukemia (CMML).
Alternate Names
Definition
Mature plasmacytoid dendritic cell proliferation (MPDCP) associated with myeloid neoplasm is a clonal proliferation of plasmacytoid dendritic cells (pDCs) with low-grade morphology identified in the context of a defined myeloid neoplasm. (WHO 5th edition).
Corresponding ICD-10-CM Codes (U.S. only)
D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissues, unspecified (effective October 01, 2015)
Sources
WHO Classification of Tumours Editorial Board. Haematolymphoid tumours. Lyon (France): International Agency for Research on Cancer; 2024. (WHO classification of tumours series, 5th ed.; vol. 11). https://publications.iarc.who.int/637.
Section: Histiocytic/dendritic cell neoplasms
Pages: Part A: 224-225
Section: Histiocytic/dendritic cell neoplasms
Pages: Part A: 224-225
