SEER Inquiry System - Question 20081003 Details

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SEER Inquiry System - Report

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Question 20081003

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Inquiry Details

References:

#1: 2007 SEER Manual, C-961. Appendix C

#2: SINQ 20071094

Question:

Reportability--Brain and CNS: For von Hippel Lindau disease with multiple hemagioblastomas, is each hemangioblastoma reportable as a new primary? See Discussion.

Discussion:

Diagnosis of von Hippel-Landau disease, multiple brain surgeries between 2002 and 2007 for recurring hemangioblastomas, 9161/1. This disease manifests as multiple (recurring) hemangioblastomas.

Answer:

For cases diagnosed 2007-2014:

If the hemagioblastomas occur in sites with different ICD-O-3 topography codes, they are separate primaries.

Please note: Rule M4 in the Benign & Borderline Intracranial and CNS Tumors MP/H coding rules on the SEER website has been corrected to read:

Tumors with ICD-O-3 topography codes that are different at the second (Cxx), third (Cxx) and/or fourth (Cxx) characters are multiple primaries.(http://www.seer.cancer.gov/tools/mphrules/benign_brain.html)

Cancer Site Category:

Brain and CNS

Data Item Category:

N/A

Other Category:

Reportability

Year:

2008