Question: 20170045

Status


Final

Category


#1:   Reportability
#2:   Brain and CNS
#3:  


References


Source 1:   ICD-O-3
pgs:  
Notes:  
Source 2:  
pgs:  
Notes:  


Question


Reportability--Brain and CNS: Is meningioangiomatosis reportable as meningiomatosis (9530/1) or angiomatous meningioma (9534/0)?  See Discussion.



Discussion


Pathology report: Brain tumor, left side: Gliotic cortex and subcortical white matter with meningioangiomatosis (see Comment). Comment This specimen represents a meningioangiomatous lesion located in the leptomeninges that projects along the Virchow-Robin spaces into the underlying cortex. The surrounding brain parenchyma demonstrates reactive changes with astrogliosis and microgliosis. An intraparenchymal neoplasm is not seen. Meningioangiomatosis is a rare benign meningovascular hamartomatous condition and usually appears in young patients.



Answer


Meningioangiomatosis is not reportable. It is a cortical lesion which may occur sporadically or in NF2 (neurofibromatosis type 2). It is not listed in ICD-O-3.



History




Last Updated


07/05/2017

Date Finalized


08/16/2017