Question: 20180071

Status


Final

Category


#1:   Solid Tumor Rules (2018)
#2:   Histology
#3:   Cervix Uteri


References


Source 1:   WHO Class Female Reproductive Organs
pgs:  
Notes:   4th edition
Source 2:  
pgs:  
Notes:  


Question


Solid Tumor Rules (2018)/Histology--Cervix uteri:  What is the correct histology code for malignant mixed Mullerian tumor (MMMT/Carcinosarcoma)?  See Discussion.



Discussion


An endometrial cancer was diagnosed in 2018. The endometrial biopsy showed malignant mixed mullerian tumor (MMMT/Carcinosarcoma). The total abdominal hysterectomy/bilateral salpingo-oophorectomy showed Endometrial Carcinosarcoma (50% serous carcinoma, 50% high grade sarcoma with rhabdomyoblastic differentiation) with invasion of 100% of the myometrium and involvement of the uterine serosa. I am not finding this in the Solid Tumor Rules or the site-specific ICD-O-3 code lists.



Answer


According to the WHO Classificationof Tumors of Female Reproductive Organs, 4th edition, MMMT (8950/3) is now a synonym for carcinosarcoma (8980/3) even though it has a separate ICD-O code. The ICD-O code for MMMT is no longer in the WHO book. Per the subject matter experts, when both terms are used in the diagnosis (carcinosarcoma/MMMT), code the histology to 8980/3. If the ONLY term used is MMMT, assign 8950/3.

The information in the 4th edition of the WHO Classification of Tumors of Female Reproductive Organs has not yet been incorporated into the Other Sites Solid Tumor Rules.



History




Last Updated


08/31/2018

Date Finalized


11/15/2018