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This neoplasm is not reportable.
Name
Lymphomatoid papulosis
ICD-O-3 Morphology
9718/1: Lymphomatoid papulosis
Effective
2010 and later
Reportability
This neoplasm is not reportable
Primary Site(s)
See Abstractor Notes
Cutaneous primary sites only (C440-C449, C510-C512, C518-C519, C600-C602, C608-C609, C632)
This hematopoietic disease is not reportable for the U.S.
Canada, refer to your specific province for reportability requirements.
This hematopoietic disease is not reportable for the U.S.
Canada, refer to your specific province for reportability requirements.
Abstractor Notes
Lymphomatoid papulosis is part of the Mature T-cell and NK-cell neoplasms lineage table in the WHO 5th edition of Hematolymphoid Tumors. (See Appendix B in the Hematopoietic Manual, Table B20)
LyP most frequently involves the trunk and extremities. The disease may have primary mucosal involvement or, rarely, can concurrently involve various mucosal and cutaneous sites.
Increased risk of a secondary cutaneous lymphoma (mycosis fungoides, primary cutaneous anaplastic large cell lymphoma). Also, at increased risk for non-hematological neoplasms such as cutaneous squamous cell carcinoma, melanoma and organ-based malignancies.
LyP most frequently involves the trunk and extremities. The disease may have primary mucosal involvement or, rarely, can concurrently involve various mucosal and cutaneous sites.
Increased risk of a secondary cutaneous lymphoma (mycosis fungoides, primary cutaneous anaplastic large cell lymphoma). Also, at increased risk for non-hematological neoplasms such as cutaneous squamous cell carcinoma, melanoma and organ-based malignancies.
Alternate Names
Lymphomatoid papulosis type A
Lymphomatoid papulosis type B
Lymphomatoid papulosis type C
Lymphomatoid papulosis type D
Lymphomatoid papulosis type E
Lymphomatoid papulosis with DUSP22 locus
Definition
Lymphomatoid papulosis (LyP) belongs to the spectrum of primary cutaneous CD30-positive T-cell lymphoproliferative disorders. It is characterized by self-healing but recurrent papulonodular skin lesions, atypical CD30-positive T cells by histology, and an excellent prognosis. (WHO 5th edition)
Genetics Data
This data item does not apply
Immunophenotyping
This data item does not apply
Corresponding ICD-10 Codes (Cause of Death codes only)
D47.7 Other specified neoplasms of uncertain or unknown behavior of lymphoid, hematopoietic, and related tissue
Corresponding ICD-10-CM Codes (U.S. only)
D47.7 Other specified neoplasms of uncertain or unknown behavior of lymphoid, hematopoietic, and related tissue (effective October 01, 2015)
Epidemiology and Mortality
Sources
WHO Classification of Tumours Editorial Board. Haematolymphoid tumours. Lyon (France): International Agency for Research on Cancer; 2024. (WHO classification of tumours series, 5th ed.; vol. 11). https://publications.iarc.who.int/637.
Section: Mature T-cell and NK-cell neoplasms
Pages: Part B: 694-697
Section: Mature T-cell and NK-cell neoplasms
Pages: Part B: 694-697
International Classification of Diseases for Oncology, 3rd edition (including revisions). Geneva: World Health Organization, 2011, 2020.
Section: ICD-O-3.2 (2020) Morphological Codes
Pages: http://www.iacr.com.fr/index.php?option=com_content&view=category&layout=blog&id=100&Itemid=577
Section: ICD-O-3.2 (2020) Morphological Codes
Pages: http://www.iacr.com.fr/index.php?option=com_content&view=category&layout=blog&id=100&Itemid=577
