This neoplasm is not reportable.

Name

Lymphomatoid papulosis

ICD-O-3 Morphology

9718/1: Lymphomatoid papulosis
Effective 2010 and later

Reportability

This neoplasm is not reportable

Primary Site(s)

See Abstractor Notes
This neoplasm is reportable for primary sites C700-C729, C751-C753 only.

Abstractor Notes

LyP is a skin-limited disease that most frequently affects the trunk and extremities. It is characterized by papular, papulo-necrotic, and/or nodular skin lesions at various stages of development. The number of lesions may vary from a few to more than a hundred.

Individual lesions disappear within 3-12 weeks and may leave behind superficial scars. The duration of the disease may vary from several months to greater than 40 years.

In 20% of patients, LyP may be preceded by, associated with, or followed by another type of malignant lymphoma, generally mycosis fungoides, cutaneous anaplastic large cell lymphoma, or Hodgkin lymphoma.

Alternate Names

LyP

Definition

Lymphomatoid papulosis (LyP) is a chronic, recurrent, self-healing skin disease that combines a usually benign clinical course with histological features suggestive of a cutaneous T-cell lymphoma.

Immunophenotyping

This data item does not apply

Corresponding ICD-9 Codes

238.79 Other lymphatic and hematopoietic tissues

Corresponding ICD-10 Codes

D47.7 Other specified neoplasms of uncertain or unknown behavior of lymphoid, hematopoietic, and related tissue

Corresponding ICD-10-CM Codes (U.S. only)

C86.6 Primary cutaneous CD30-positive T-cell proliferations (effective October 01, 2015)

Sources

Swerdlow SH, Campo E, Harris NL, Jaffe ES, Pileri SA, Stein H, Thiele J (Eds):
WHO Classification of Tumours of Haematopoietic and Lymphoid Tissues (Revised 4th edition)
IARC: Lyon 2017
Section: Section: Mature T- and NK-cell neoplasms
Pages: Pages: 392-395

International Classification of Diseases for Oncology, Third Edition, Second Revision. Geneva: World Health Organization, 2020
Section: ICD-O-3.2 (2020) Morphological Codes
Pages: http://www.iacr.com.fr/index.php?option=com_content&view=category&layout=blog&id=100&Itemid=577
Glossary