Interdigitating dendritic cell sarcoma
Help me code for diagnosis year :
Rare sarcoma arising from the interdigitating reticulum cells in the T-cell area of the lymph node and forming a node-based tumor.
Indeterminate cells are the proposed precursor of Langerhans cells, so this malignancy is in myeloid-derived dendritic cells in contrast to fibroblastic reticular cell tumor (9759/3). These lesions are usually based in the dermis but may extend into the subcutaneous fat. The infiltrate is diffuse, comprising cells resembling Langerhans cells.
Visceral organs that are commonly affected include the liver, spleen, kidney and lung. Stage may be an important prognostic factor; however, histological features have not been correlated with clinical outcome.
Indeterminate dendritic cell tumor is a variant of interdigitating dendritic cell sarcoma that should also be coded 9757/3. The clinical course has been highly variable, ranging from spontaneous regression to rapid progression.