SEER Inquiry System - Question 20130147 Details

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Produced: 08/27/2025 3:17 AM

Question 20130147

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Inquiry Details

References:

Heme & Lymph Manual & DB

Question:

Primary site--Heme & Lymphoid Neoplasms: What the primary site for a diagnosis of Langerhans cell histiocytosis with multifocal multisystem involvement of the skin, chest, CNS and thyroid, but no evidence of involvement on a bone scan?

Discussion:

Answer:

For cases diagnosed 2010 and forward, access the Hematopoietic Database at http://seer.cancer.gov/seertools/hemelymph.

Code the primary site to C809 [unknown].

Langerhans Cell Histiocytosis (LCH) includes three major groups:

Unifocal: Slowly progressing disease, involves one organ.

Multifocal unisystem: Involves several organs in one system.

Multifocal multisystem: Involves several organs in two or more systems.

When the disease is both multifocal and multisystem, code the primary site to unknown [C809] because there is no way to identify the origin of the neoplasm in this situation.

SEER*Educate provides training on how to use the Heme Manual and DB. If you are unsure how to arrive at the answer in this SINQ question, refer to SEER*Educate to practice coding hematopoietic and lymphoid neoplasms. Review the step-by-step instructions provided for each case scenario to learn how to use the application and manual to arrive at the answer provided. https://educate.fhcrc.org/LandingPage.aspx.

Cancer Site Category:

Heme & Lymphoid Neoplasms

Data Item Category:

Primary site

Other Category:

N/A

Year:

2013