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SEER Inquiry System - Report
Produced: 11/21/2024 7:37 PM
Question 20240041
Inquiry Details
References:
#1: Solid Tumor Rules. Non-Malignant CNS 2024 Update
#2: WHO Class Eye Tumors, 139-140. 4th edition
Question:
Reportability--Brain and CNS: Is an optic nerve meningioma reportable if stated to arise in the “intraorbital segment” of the optic nerve meninges? See Discussion.
Discussion:
Patient was diagnosed on imaging with enhancement along the right optic nerve intraorbital segment, displacing the optic nerve, most consistent with optic nerve sheath meningioma.
Extracranial meningiomas are rare, however SINQ 20230052 does contain an exception for reportability in a different head and neck site because it is not an intracranial location.
It is unclear if this portion of the meninges surrounding the intraorbital optic nerve is still “intracranial” and thus reportable.
Answer:
Report optic nerve sheath meningioma arising in the intraorbital segment. The optic nerve contains four segments, of which intraorbital is one. The WHO Classification of Eye Tumors, 4th edition, defines meningioma as a neoplasm originating from the meningothelial cells of the optic nerve leptomeninges. According to the Table 3 of the Non-malignant Solid Tumor Rules, all portions of the optic are reportable and meningiomas arising in the dura/meninges of an intracranial nerve are coded to cerebral meninges C700.
